Search on: SYSTEMIC CAPILLARY LEAK SYNDROME 
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Descriptor English:   Capillary Leak Syndrome 
Descriptor Spanish:   Síndrome de Fuga Capilar 
Descriptor Portuguese:   Síndrome de Vazamento Capilar 
Synonyms English:   Capillary Leak Syndromes
Clarkson Disease
Clinical Capillary Leak Syndrome
Systemic Capillary Leak Syndrome  
Tree Number:   C14.907.218
Definition English:   A condition characterized by recurring episodes of fluid leaking from capillaries into extra-vascular compartments causing hematocrit to rise precipitously. If not treated, generalized vascular leak can lead to generalized EDEMA; SHOCK; cardiovascular collapse; and MULTIPLE ORGAN FAILURE. 
See Related English:   Endoleak
Multiple Organ Failure
 
History Note English:   1997 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   32962 
Unique Identifier:   D019559 

Occurrence in VHL:
 

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